Contributing Authors v
Preface vii
Acknowledgments ix
Introduction xiii
1 The Basic Defect 1
Daniel J. Weiner, Raymond A. Frizzell, and David M. Orenstein
2 Making the Diagnosis 13
Jonathan E. Spahr, David M. Orenstein, and Daniel J. Weiner
3 The Respiratory System 21
Daniel J. Weiner and David M. Orenstein
4 The Gastrointestinal Tract 83
Douglas S. Lindblad, Daniel J. Weiner, and David M. Orenstein
5 Other Systems 103
Daniel J. Weiner and David M. Orenstein
6 Nutrition 113
Judith A. Fulton, Iris Yann, Daniel J. Weiner, and David M. Orenstein
7 Hospitalization and Other Special Treatments 135
Jonathan E. Spahr, David M. Orenstein, Daniel J. Weiner,
and Louise T. Bauer
8 Transplantation 153
Geoffrey Kurland, Jonathan E. Spahr, Daniel J. Weiner,
and David M. Orenstein
9 Daily Life 195
Jonathan E. Spahr, David M. Orenstein, and Daniel J. Weiner
10 Exercise 205
David M. Orenstein and Daniel J. Weiner
11 Genetics 221
Barbara Karczeski, Garry R. Cutting, and David M. Orenstein
12 The Family 235
David M. Orenstein and Daniel J. Weiner
13 The Teenage Years 245
Jonathan E. Spahr, David M. Orenstein, and Daniel J. Weiner
14 Cystic Fibrosis and Adulthood 265
Joseph M. Piliewski, David M. Orenstein, Jonathan E. Spahr,
and Daniel J. Weiner
15 Death and Cystic Fibrosis 287
Elisabeth P. Dellon and David M. Orenstein
16 Research and Future Treatments 295
Christopher Penland, David M. Orenstein, and Daniel J. Weiner
17 The Cystic Fibrosis Foundation 311
Robert J. Beall
A P P E N D I C E S
A Glossary of Terms 319
B Medications 325
C Airway Clearance Techniques 363
D Some High Calorie Recipes 375
E The History of Cystic Fibrosis 385
F Bibliography and Resources 387
G Cystic Fibrosis Care Centers in the United States 391
H Cystic Fibrosis Care Centers Worldwide 411
Index 445
